Clin Surg | Volume 2, Issue 1 | Case Report | Open Access

Right Sided Reconstruction of the Heart for Invasive Angiosarcoma of the Right Atrium

Elien Brouwers1, Marie-Christine Herregods1, Eric Verbeken2, Paul Herijgers3 and Wouter Oosterlinck3*

1Department of Cardiovascular Diseases, Cardiology, University Hospitals Leuven, Belgium
2Department of Imaging and Pathology, University Hospitals Leuven, Belgium
3Department of Cardiovascular Diseases, research unit of Cardiac Surgery, University Hospitals Leuven, Belgium

*Correspondance to: Wouter Oosterlinck 

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Abstract

A 35-year old male presented with new diagnosis of cardiac angiosarcoma. We describe the case, diagnosis, treatment modalities and first observations concerning survival. Overall, cardiac sarcomas are a rare entity. There are several subtypes of sarcomas and the angiosarcoma is the most common type of heart sarcomas in adults, especially in male population. The symptoms of cardiac sarcomas are non-specific and depend on the size of the tumor, the anatomical localization, the myocardial involvement and the presence of metastatic disease. Dyspnea is the most common symptom by diagnosis. The number of angiosarcomas diagnosed, has increased since non-invasive imaging (echocardiography, MRI, CT) has improved in quality.Final diagnosis can only be made by cytological and immunohistochemical examination.Once the diagnosis has been established, the therapy has to be started as soon as possible. Most important in the treatment of sarcomas is a complete surgical resection, as this gives the most successful disease-free survival. Until now, the role of chemotherapy is unclear. Unfortunately, the prognosis of cardiac sarcomas is poor.The median time to relapse is longer in patients with angiosarcoma than other sarcomas.

Keywords:

Angiosarcoma; Cardiac malignancy; Cardiac tumor; Diagnosis; Treatment

Citation:

Brouwers E, Herregods M-C, Verbeken E, Herijgers P, Oosterlinck W. Right Sided Reconstruction of the Heart for Invasive Angiosarcoma of the Right Atrium. Clin Surg. 2017; 2: 1460.

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